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Keywords = keratinization disorder
Number of Articles: 2
Bullous ichthyosiform erythroderma
Volume 16, Issue 3 , 2013, , Pages 112-115
Abstract
Bullous ichthyosiform erythroderma (BIE) is a rare disorder of keratinization (mutations in either keratin 1 or 10). It typically presents with fragile skin, which gives way to gradual evolutionof hyperkeratosis. Flaccid blisters, peeling, and superficial erosions at sites of minor trauma ... Read MorePapillon-Lefevre syndrome: A report of two cases in a family
Volume 9, suppl.1 , 2006, , Pages 1-1