TY - JOUR ID - 98173 TI - Phakomatosis pigmentovascularis type IIa JO - Iranian Journal of Dermatology JA - IJD LA - en SN - AU - Abbas, Rasi AU - Mehdi, Tabaie AU - Habib, Hassannejad AD - Y1 - 2012 PY - 2012 VL - 15 IS - 2 SP - 62 EP - 65 KW - nevus of Ota KW - phakomatosis pigmentovascularis KW - pigmentary anomalies KW - port-wine stains KW - vascular anomalies DO - N2 - Phakomatosis Pigmentovascularis (PPV) is a rare cutaneous congenital malformation syndrome, defined as simultaneous occurrence of congenital cutaneous vascular and pigmentary anomalies. As most of the reported cases are from Far East countries, especially Japan, we reported a case of PPV type IIa in an Iranian patient. This case was unusual because of the coexistence of unilateral extensive port-wine stains all over the left body side and left hard palate and a right plantar port-wine stain. UR - https://www.iranjd.ir/article_98173.html L1 - https://www.iranjd.ir/article_98173_11269f6cc61acf9ff4e6ce5c6200b011.pdf ER -