TY - JOUR ID - 99712 TI - Bullous ichthyosiform erythroderma JO - Iranian Journal of Dermatology JA - IJD LA - en SN - AU - Mohammadzadeh Shanehsaz, Siavash AU - Bittar, Roshan AU - Anis, Abdollah AU - Ishkhanian, Silva AD - Y1 - 2013 PY - 2013 VL - 16 IS - 3 SP - 112 EP - 115 KW - bullous ichthyosiform erythroderma KW - hystrix KW - keratinization disorder DO - N2 - Bullous ichthyosiform erythroderma (BIE) is a rare disorder of keratinization (mutations in either keratin 1 or 10). It typically presents with fragile skin, which gives way to gradual evolutionof hyperkeratosis. Flaccid blisters, peeling, and superficial erosions at sites of minor trauma or friction are apparent within the first few hours of life. Yellow-brown, waxy, ridged or corrugatedscales build up in skin creases, sometimes forming spiny (Hystrix) outgrowths. Cobble stone-like keratoses occur at other sites such as the dorsal aspects of the hands and feet and over the trunk.We report an 11-year-old boy with a generalized hyperkeratosis on the neck, trunk, extremities, and scalp. UR - https://www.iranjd.ir/article_99712.html L1 - https://www.iranjd.ir/article_99712_eb1b768322dd19b99986deecfd728597.pdf ER -