Document Type : Case Report



Porokeratosis (PK) is an uncommon disorder of epidermal keratinization characterized by annular plaques with an atrophic center surrounded by a raised, keratotic wall, with unknown aetiology and an unpredictable outcome. It has several clinical forms including porokeratosis of Mibelli, giant porokeratosis, linear porokeratosis, disseminated superficial actinic porokeratosis, palmoplantar porokeratosis and punctate porokeratosis.
Genital porokeratosis is a rare and probably underestimated subset of PK that mostly affects middle-aged men. Although there are many clinical variants, coexistence of different variants of porokeratosis in a single patient has been regarded as a rare occurrence. Here we report a rare variant of porokeratosis , genital or ptychotropica porokeratosis, accompanied by superficial actinic porokeratosis in a patient and his family members.