Nevus lipomatosus superficialis (NLS) is a hamartomatous skin lesion defined by the presence of mature adipose tissues among the collagen bundles of the dermis. It is classified into two forms:
the classical form and the solitary form. The classical NLS most commonly involves the pelvic or gluteal region. In this paper, we report a case of classical NLS over the neck because of its atypical
site. In addition, our patient had some uncommon features of NLS such as the presence of comedo-like lesions on the plaque and a foul-smelling discharge.