Document Type : Case Report


Department of Dermatology, Venereology and Leprosy, Sri Manakula Vinayagar Medical College and Hospital, Puducherry, India


Porokeratosis is a heterogeneous group of keratinization disorders
with an autosomal dominant inheritance pattern. The etiology and
pathogenesis of this disease have not been completely elucidated.
The porokeratosis clinically presents with a characteristic prominent
peripheral ridge and central dell. The histological feature of the
parakeratotic column known as ‘cornoid lamellae’ is a hallmark
feature observed in the peripheral rim. Among the various
morphological forms, linear porokeratosis is a rare variant with
four subtypes. When compared to other forms, the linear variant
carries an increased risk of malignancy, particularly squamous
cell carcinoma, warranting a regular follow-up. Though there are
multiple treatment options, achieving complete clinical resolution
is difficult. We report an interesting case of linear porokeratosis
with generalized lesions in a 60-year-old male. The lesions were
typical and predominantly distributed in the extremities. The
biopsy was diagnostic in our patient. This case is reported for
its rare presentation and clinical interest.