Linear epidermal nevi frequently follow the lines of Blaschko and may be confused with the verrucous stage of incontinentia pigmenti. Inflammatory epidermal nevus appears as a line array of pink to red papules usually on the lower limb (Buttock and hip) clinically resembling psoriasis or eczematous dermatitis. But inflammatory epidermal nevus has distinct histopathologic features. We report a case of a 12-year-old Iranian girl who had a huge verrucous lesion on left lower limb since age of 4 years. Bone age of the patient was 6 years and her left lower limb was 6 centimeters longer than right side. Her lesion was excised in several sessions and grafted but showed recurrence.